biostudies-literatureUnknown18(6)Ouaissi M<h4>Aim</h4>To compare clinical presentation, operative management and short- and long-term outcomes of congenital bile duct cysts (BDC) in adults with children.<h4>Methods</h4>Retrospective multi-institutional Association Francaise de Chirurgie study of Todani types I+IVB and IVA BDC.<h4>Results</h4>During the 37-year period to 2011, 33 centers included 314 patients (98 children; 216 adults). The adult population included more high-risk patients, with more active, more frequent prior treatment (47.7% vs 11.2%; p < 0.0001), more complicated presentation (50.5% vs 35.7%; p = 0.015), more synchronous biliary cancer (11.6% vs 0%; p = 0.0118) and more major surgery (23.6% vs 2%; p < 0.0001), but this latter feature was only true for type I+IVB BDC. Compared to children, the postoperative morbiHPB : the official journal of the International Hepato Pancreato Biliary Association529-39https://www.ebi.ac.uk/biostudies/studies/S-EPMC4913142biostudies-literatureCongenital bile duct cyst (BDC) is a more indolent disease in children compared to adults, except for Todani type IV-A BDC: results of the European multicenter study of the French Surgical Association.PMC4913142Meurisse NBentabak KMolle GBaulieux JSauvanet ADubois RPruvot FRRisse OCapussotti LGeiss SMure PYGauthier FKianmanesh RDuguet LDucerf CDane CTHubert CBranchereau SGiulante FMartelli HDemartines NMsika SFarges ODoussot AWildhaber BRoux ABoudjema KArdito FGigot JFLebeau RFalconi MRevillon YVibert EAyav ACollet DGraba ANuzzo GLerut JHardwigsen JFrench Surgical AssociationBalladur PCristaudi AAdam RTruant SRinaudo MLaurent ASalloum CLangelle SSarnacki SLaurain CAMansvelt BRat PCastaing DCherqui DGelas TAlhassane TVanlander ASa Cunha Ade Goyet Jde VPaye FTroisi RHalkic NCompagnon PMabrut JYIrtan SReding RPartensky CSaviano MPirenne JAdham MRoberta GAzoulay DOrtega-Deballon PChafik BRagot EBouchoucha SOtte JBLe Treut YPBaraket OLetoublon CPalot JPOuaissi MWassila OBoleslawski ESommacale DSastre BCiacio OBelghiti JDe Taffin GCorfiotti FAgostino Mde RGouillat CfalseCongenital bile duct cyst (BDC) is a more indolent disease in children compared to adults, except for Todani type IV-A BDC: results of the European multicenter study of the French Surgical Association.<h4>Aim</h4>To compare clinical presentation, operative management and short- and long-term outcomes of congenital bile duct cysts (BDC) in adults with children.<h4>Methods</h4>Retrospective multi-institutional Association Francaise de Chirurgie study of Todani types I+IVB and IVA BDC.<h4>Results</h4>During the 37-year period to 2011, 33 centers included 314 patients (98 children; 216 adults). The adult population included more high-risk patients, with more active, more frequent prior treatment (47.7% vs 11.2%; p < 0.0001), more complicated presentation (50.5% vs 35.7%; p = 0.015), more synchronous biliary cancer (11.6% vs 0%; p = 0.0118) and more major surgery (23.6% vs 2%; p < 0.0001), but this latter feature was only true for type I+IVB BDC. Compared to children, the postoperative morbi2016-01-01T00:00:00Z2016 Jun2025-04-04T07:28:44.237Z2019-03-27T02:16:25ZS-EPMC49131422731795810.1016/j.hpb.2016.04.005