Dataset Information

Hemidystonia secondary to pediatric thalamic glioblastoma: a case report.

ABSTRACT:

Introduction

Thalamic tumors are rare and uncommonly manifest as movement disorders, including hemidystonia. Despite this association, little is known about the evolution of hemidystonia.

Case description

We report on a 11-year-old boy who complained of hypaesthesia and fine motor problems in the left hand. A magnetic resonance imaging showed a large mass in the right thalamus. Stereotactic biopsy revealed a WHO grade 4 astrocytoma, and the patient underwent normofractioned radiochemotherapy with proton-beam radiation and temozolomide. Three months later, a spastic hemiparesis developed on the left side, which progressed over months. Over the following months, the hemiparesis slowly improved, but hemidystonia in the same side developed. This was accompanied with radiological evidence of tumor regression, showing a persistent lesion in the ventral posterolateral and the intralaminar thalamus.

Conclusion

This case illustrates the unusual and complex temporal course of appearance and disappearance of hemidystonia along with the regression and growth in glioblastoma involving the thalamus.

SUBMITTER: Wolff Fernandes F

PROVIDER: S-EPMC10006018 | biostudies-literature | 2023 Feb

REPOSITORIES: biostudies-literature

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Publications

Hemidystonia secondary to pediatric thalamic glioblastoma: a case report.

Wolff Fernandes Filipe F Saryyeva Assel A Ertl Philipp P Krauss Joachim Kurt JK

Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery 20221012 2

<h4>Introduction</h4>Thalamic tumors are rare and uncommonly manifest as movement disorders, including hemidystonia. Despite this association, little is known about the evolution of hemidystonia.<h4>Case description</h4>We report on a 11-year-old boy who complained of hypaesthesia and fine motor problems in the left hand. A magnetic resonance imaging showed a large mass in the right thalamus. Stereotactic biopsy revealed a WHO grade 4 astrocytoma, and the patient underwent normofractioned radioc ...[more]

PMID: 36220936

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Project description:Introduction and importance Component separation technique is utilized in adults to repair large abdominal wall defects but rarely used in children. We report a successfully performed component separation technique in a child after neonatal Gross closure for large omphalocele without biologic mesh placement. Case presentation A 6-year-old girl was treated at the age of 4 days for omphalocele type 2 according to Gross technique. She reconsulted six years later. Clinical examination showed a large eventration measuring 150 ∗ 100 mm. CT scan revealed a broad collar of 150 mm and a large pocket containing liver, transverse colon, stomach and part of the small intestine. The child was proposed for a cure of the eventration using synthetic mesh type GORTEX. Intraoperatively, releasing bowel adhesions with abdominal wall resulted in perforation of the small intestine. Faced with the inability to use the mesh we resorted to abdominal closure with component separation technique. The postoperative was simple without complications or recurrence of the eventration. Follow up was of 4 years. Clinical discussion Staged surgical closure and non-operative delayed closure are the two distinct strategies for managing giant omphaloceles. By providing closure with less intra-abdominal pressure, the Component separation technique is a procedure which can be used in the two strategies. It may minimize the complications associated with large omphalocele management. Conclusion Faced with the impossibility of using a mesh, the component separation technique must be recognized as part of the therapeutic arsenal for secondary closure in children with a giant omphalocele. Highlights • We report a case of a secondary closure of large omphalocele using component separation technique in 12 years-old girl.• Our pediatric patient illustrates the safety and feasibility of this technique in children without any complication.• Component separation technique must be recognized in the therapeutic arsenal closure of large abdominal wall defect in children

Dataset Information

Hemidystonia secondary to pediatric thalamic glioblastoma: a case report.

Introduction

Case description

Conclusion

Publications

Hemidystonia secondary to pediatric thalamic glioblastoma: a case report.

Similar Datasets

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