Hypertrophic olivary degeneration associated with bilateral vocal cord adductor dystonia.

ABSTRACT:

Background

Hypertrophic olivary degeneration (HOD) is a rare condition caused by lesions within the dentato-rubro-olivary pathway, resulting in ocular nystagmus and palatal myoclonus (oculopalatal tremor) but not usually dystonia. Dystonia is an uncommon association, and we present the first reported association of hypertrophic olivary degeneration with bilateral vocal cord dystonia.

Case presentation

A 33 year old male presented initially with acute hydrocephalus on the background of previous ventriculoperitoneal (VP) shunting for previously treated medulloblastoma. After revision of the VP shunt, the patient developed progressive hiccups and stridor leading to respiratory failure requiring intubation. Ocular pendular nystagmus and palatal myoclonus at 3 Hz was observed. Fl

SUBMITTER: Lycett M 

PROVIDER: S-EPMC10012681 | biostudies-literature | 2023 Mar

REPOSITORIES: biostudies-literature