What Is Hemidystonia?

ABSTRACT:

Background

Hemidystonia is defined as dystonia restricted to one side of the body. It is traditionally believed to result from a lesion in the contralateral hemisphere.

Objectives

To describe a series of hemidystonia patients without lesions on brain imaging.

Methods

We searched for individuals with potential hemidystonia who were included in the Dystonia Coalition or Movement Disorder Society Genetic mutation database (MDSgene), and conducted a systematic review.

Results

We found 10 individuals classified as hemidystonia or with homolateral limb dystonia among 3696 cases enrolled by the Dystonia Coalition, 9 cases in MDSgene, and one idiopathic case in the literature. None had evidence of a brain lesion. Body distributions used to define hemidystonia varied co

SUBMITTER: Vizcarra JA 

PROVIDER: S-EPMC10026294 | biostudies-literature | 2023 Mar

REPOSITORIES: biostudies-literature