Junctional rhythm produces retrograde flow in the whole Fontan system: cardiac magnetic resonance-derived flow documentation-a case report.

ABSTRACT:

Background

Arrhythmias after palliation of congenital malformations with functional monoventricle by different Fontan modifications are very common. Sinus node dysfunction and junctional rhythm are known to have a high prevalence and a detrimental impact on the optimal functioning of Fontan circulations. Maintaining sinus node function has high prognostic significance, and some cases have even been described where atrial pacing with restoring of atrioventricular synchrony was able to reverse protein-losing enteropathy with overt failure of the Fontan.

Case summary

A 12-year-old boy with a complex congenital malformation (double outlet right ventricle, transposition of the great arteries, pulmonary stenosis, and straddling atrioventricular valve) palliated through a modified

SUBMITTER: Ferrari I 

PROVIDER: S-EPMC10061559 | biostudies-literature | 2023 Mar

REPOSITORIES: biostudies-literature