Use of disease assessment tools to increase the value of case reports on Susac syndrome: two case reports.

ABSTRACT:

Background

Susac syndrome is an immune-mediated, ischemia-producing, occlusive microvascular endotheliopathy that threatens the brain, retina, and inner ear. There is a need for disease assessment tools that can help clinicians and patients to more easily, accurately, and uniformly track the clinical course and outcome of Susac syndrome. Ideally, such tools should simultaneously facilitate the clinical care and study of Susac syndrome and improve the value of future case reports. To meet this need, two novel clinical assessment tools were developed: the Susac Symptoms Form and the Susac Disease Damage Score. The former is a comprehensive self-report form that is completed by patients/families to serially document the clinical status of a patient. The latter documents the extent of

SUBMITTER: Bullock DR 

PROVIDER: S-EPMC10097450 | biostudies-literature | 2023 Apr

REPOSITORIES: biostudies-literature