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Detection and significance of glial fibrillary acidic protein antibody in autoimmune astocytopathy and related diseases.


ABSTRACT: Autoimmune glial fibrillary acidic protein astrocytopathy (GFAP-A) is an antibody-related astrocytic disease for which a specific GFAP antibody serves as a biological marker. Indeed, cerebral spinal fluid positive and/or seropositivity for GFAP is an important basis for its diagnosis. However, because patients with autoimmune encephalitis or demyelinating diseases can have a similar antibody profile, termed overlapping autoimmune syndrome, it remains a challenge for clinicians to diagnose and suitably classify autoimmune GFAP-A. To further understand the significance of GFAP antibody detection in neuroimmune diseases, this article discusses GFAP antibodies in autoimmune GFAP-A, progress for detection of GFAP antibodies, diagnostic significance of GFAP antibodies in prototypical disease, as well as overlapping syndrome.

SUBMITTER: Huang J 

PROVIDER: S-EPMC10116425 | biostudies-literature | 2023 Apr

REPOSITORIES: biostudies-literature

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Detection and significance of glial fibrillary acidic protein antibody in autoimmune astocytopathy and related diseases.

Huang Jiehong J   Huang Wenyao W   Zhou Ruisi R   Lin Wenhui W   Chen Ting T   Long Youming Y  

Annals of translational medicine 20190805 7


Autoimmune glial fibrillary acidic protein astrocytopathy (GFAP-A) is an antibody-related astrocytic disease for which a specific GFAP antibody serves as a biological marker. Indeed, cerebral spinal fluid positive and/or seropositivity for GFAP is an important basis for its diagnosis. However, because patients with autoimmune encephalitis or demyelinating diseases can have a similar antibody profile, termed overlapping autoimmune syndrome, it remains a challenge for clinicians to diagnose and su  ...[more]

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