Ontology highlight
ABSTRACT:
SUBMITTER: Balaban DT
PROVIDER: S-EPMC10244657 | biostudies-literature | 2023
REPOSITORIES: biostudies-literature
Balaban Denis T DT Hutto Spencer K SK Panzarini Bruno P BP O'Shea Aileen A Varma Aditi A Jones Pamela S PS Chwalisz Bart K BK Stone John H JH Venna Nagagopal N
Frontiers in neurology 20230524
IgG4-related disease-associated hypertrophic pachymeningitis (IgG4RD-HP) is a fibroinflammatory autoimmune disorder in which diagnosis is difficult without biopsy. Guidance on management of disease refractory to glucocorticoids and intravenous rituximab is limited. We present the case of a 68-year-old woman with IgG4RD-HP who developed sensorineural hearing loss with associated bulky basilar pachymeningeal enhancement. Her cerebrospinal fluid was inflammatory and had an elevated IgG4 concentrati ...[more]