Dataset Information

Rectal atresia and rectal stenosis: the ARM-Net Consortium experience.

ABSTRACT:

Purpose

To assess the number, characteristics, and functional short-, and midterm outcomes of patients with rectal atresia (RA) and stenosis (RS) in the ARM-Net registry.

Methods

Patients with RA/RS were retrieved from the ARM-Net registry. Patient characteristics, associated anomalies, surgical approach, and functional bowel outcomes at 1 and 5-year follow-up were assessed.

Results

The ARM-Net registry included 2619 patients, of whom 36 (1.3%) had RA/RS. Median age at follow-up was 7.0 years (IQR 2.3-9.0). Twenty-three patients (63.9%, RA n = 13, RS n = 10) had additional anomalies. PSARP was the most performed reconstructive surgery for both RA (n = 9) and RS (n = 6) patients. At 1-year follow-up, 11/24 patients with known data (45.8%, RA n = 5, RS n = 6) were constipated, of whom 9 required stool softeners and/or laxatives. At 5-year follow-up, 8/9 patients with known data (88.9%, RA n = 4, RS n = 4) were constipated, all requiring laxatives and/or enema.

Conclusion

RA and RS are rare types of ARM, representing 1.3% of patients in the ARM-Net registry. Additional anomalies were present in majority of patients. Different surgical approaches were performed as reconstructive treatment, with constipation occurring in 46% and 89% of the patients at 1 and 5-year follow-up. However, accurate evaluation of long-term functional outcomes remains challenging.

SUBMITTER: de Beaufort CMC

PROVIDER: S-EPMC10382331 | biostudies-literature | 2023 Jul

REPOSITORIES: biostudies-literature

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Publications

Rectal atresia and rectal stenosis: the ARM-Net Consortium experience.

de Beaufort Cunera M C CMC Gorter Ramon R RR Iacobelli Barbara D BD Midrio Paola P Sloots Cornelius E J CEJ Samuk Inbal I van Rooij Iris A L M IALM Lisi Gabriele G

Pediatric surgery international 20230728 1

<h4>Purpose</h4>To assess the number, characteristics, and functional short-, and midterm outcomes of patients with rectal atresia (RA) and stenosis (RS) in the ARM-Net registry.<h4>Methods</h4>Patients with RA/RS were retrieved from the ARM-Net registry. Patient characteristics, associated anomalies, surgical approach, and functional bowel outcomes at 1 and 5-year follow-up were assessed.<h4>Results</h4>The ARM-Net registry included 2619 patients, of whom 36 (1.3%) had RA/RS. Median age at foll ...[more]

PMID: 37507508

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Dataset Information

Rectal atresia and rectal stenosis: the ARM-Net Consortium experience.

Purpose

Methods

Results

Conclusion

Publications

Rectal atresia and rectal stenosis: the ARM-Net Consortium experience.

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