Case report: Unilateral pulmonary artery agenesis and Kommerell's diverticulum in 1-year old girl

ABSTRACT:

Background

Unilateral pulmonary artery agenesis (UPAA) and Kommerell's diverticulum (KD) are two rare embryologically unrelated congenital vascular malformations rarely diagnosed in children. This is the first report of our knowledge of the unique combination for a child as patients are at a high risk of pulmonary hypertension and rupture of the diverticulum. Our aim is to present the case of a pediatric patient with UPAA and KD with the short literature review and to highlight the importance of early diagnostics of rare congenital vascular malformations.

Case report

A 1-year-old girl presented to the emergency department with prolonged cough and variable wheezing. A hypoplastic left lung was suspected in the radiographic image of the chest. A transthoracic echocardiogram

SUBMITTER: Miseviciene V 

PROVIDER: S-EPMC10424440 | biostudies-literature | 2023 Jan

REPOSITORIES: biostudies-literature