Chronic constrictive pericarditis: a rare cardiac involvement in primary Sjogren's syndrome.

ABSTRACT:

Background

Constrictive pericarditis represents a chronic condition and systemic inflammatory diseases are a known, yet uncommon, cause. Pericardial involvement is seldom reported in primary Sjögren's syndrome, usually occurring in association with pericardial effusion or pericarditis. We report a case of constrictive pericarditis with an insidious course and unusual evolution associated with primary Sjögren's syndrome. Due to the challenging nature of the diagnosis, clinical suspicion and multimodality imaging are essential for early identification and prompt initiation of treatment. Long-term outcomes remain uncertain. To the best of our knowledge, no other cases linking this autoimmune disease to constrictive pericarditis have been reported.

Case presentation

We present t

SUBMITTER: Duarte F 

PROVIDER: S-EPMC10512490 | biostudies-literature | 2023 Sep

REPOSITORIES: biostudies-literature