The Many Faces of Arrhythmogenic Cardiomyopathy: An Overview.
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ABSTRACT:
SUBMITTER: Tadros HJ
PROVIDER: S-EPMC10625769 | biostudies-literature | 2023
REPOSITORIES: biostudies-literature
Publications
The Many Faces of Arrhythmogenic Cardiomyopathy: An Overview.
Tadros Hanna J HJ Miyake Christina Y CY Kearney Debra L DL Kim Jeffrey J JJ Denfield Susan W SW
The application of clinical genetics 20231101
Arrhythmogenic cardiomyopathy (AC) is a disease that involves electromechanical uncoupling of cardiomyocytes. This leads to characteristic histologic changes that ultimately lead to the arrhythmogenic clinical features of the disease. Initially thought to affect the right ventricle predominantly, more recent data show that it can affect both the ventricles or the left ventricle alone. Throughout the recent era, diagnostic modalities and criteria for AC have continued to evolve and our understand ...[more]
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