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Case Report: One heart with two lobes: a rare infantile congenital giant left atrial appendage aneurysm.

ABSTRACT: Left atrial appendage aneurysm (LAAA) is an extremely rare congenital heart abnormality, with varying degrees of symptoms, ranging from asymptomatic to arrhythmia, thromboembolic event or airway obstruction. Most infantile cases were incidentally found by echocardiography. Contrast-enhanced chest tomography can confirm the diagnosis and inform surgical plan. We describe an asymptomatic young female infant who had a unique extreme cardiomegaly on a chest x-ray and received surgical aneurysmectomy. Her heart was restored to a normal cardiac size after the heart surgery.

SUBMITTER: Chan YJ

PROVIDER: S-EPMC10694266 | biostudies-literature | 2023

REPOSITORIES: biostudies-literature

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Case Report: One heart with two lobes: a rare infantile congenital giant left atrial appendage aneurysm.

Chan Yu-Jen YJ Ly Ly Nguyen Thi NT Hai Nguyen Minh NM Jan Sheng-Ling SL

Frontiers in pediatrics 20231120

Left atrial appendage aneurysm (LAAA) is an extremely rare congenital heart abnormality, with varying degrees of symptoms, ranging from asymptomatic to arrhythmia, thromboembolic event or airway obstruction. Most infantile cases were incidentally found by echocardiography. Contrast-enhanced chest tomography can confirm the diagnosis and inform surgical plan. We describe an asymptomatic young female infant who had a unique extreme cardiomegaly on a chest x-ray and received surgical aneurysmectomy ...[more]

PMID: 38054189

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