The challenging approach of a young patient with a primary intimal sarcoma of the heart: a case report.

ABSTRACT:

Background

Primary intimal sarcomas of the heart are extremely rare and have a dismal prognosis. Their management represents a complex clinical challenge since complete surgical resection is the only reliable possibility of cure but is only possible in 50% of patients. In non-resectable disease, anthracycline-based therapy is the most effective treatment, but pazopanib may be used in patients unfit to receive anthracyclines.

Case summary

A 38-year-old man presented with acute right heart failure symptoms due to a primary intimal sarcoma of the heart. A definite diagnosis was made after cardiac surgery. Multi-modality cardiac imaging showed early recurrence of disease with mitral valve and pulmonary veins' invasion, and the patient was deemed inoperable. Due to chronic kidney

SUBMITTER: Martinho M 

PROVIDER: S-EPMC10875919 | biostudies-literature | 2024 Feb

REPOSITORIES: biostudies-literature