A large type I right pulmonary artery to left atrium fistula: underwent successful percutaneous device closure with duct occluder-a rare case report.

ABSTRACT:

Background

Pulmonary artery to left atrium fistula is an unusual structural cause of silent cyanosis. Only less than 100 cases have been reported so far. A high index of clinical suspicion and proper evaluation with bubble contrast echocardiography and cardiac computed tomography (CT) will help to detect this treatable anomaly. The advent of safer percutaneous closure methods has replaced the need for more invasive surgical closure.

Case presentation

We report an adolescent boy, who presented with long-standing cyanosis and progressive dyspnea with normal clinical cardiovascular examination. On evaluation, echocardiography and bubble contrast study revealed a large right pulmonary artery (RPA) to left atrium (LA) fistula. Cardiac CT confirmed the same with normal pulmonary v

SUBMITTER: Vinothkumar SP 

PROVIDER: S-EPMC10881914 | biostudies-literature | 2024 Feb

REPOSITORIES: biostudies-literature