Patch aortoplasty for supravalvular aortic stenosis in an adult patient: A case report.

ABSTRACT:

Introduction

Supravalvular aortic stenosis (SVAS) is an uncommon congenital abnormality that presents with intimal thickening of the aortic media at the sinotubular junction. Given the congenital nature of the disease, patients usually become symptomatic in childhood.

Presentation of case

A 48-year-old man developed symptomatic SVAS in middle age. A patch aortoplasty with a bovine pericardial patch was performed. His postoperative course was uneventful, and echocardiography revealed a significant decrease in peak velocity and pressure gradient.

Discussion

SVAS, a congenital heart disease with an incidence of 1 in 20,000 live births, is often linked to Williams syndrome but can also occur independently. Isolated SVAS is generally less severe and may not show symptoms i

SUBMITTER: Arai A 

PROVIDER: S-EPMC10943428 | biostudies-literature | 2024 Mar

REPOSITORIES: biostudies-literature