Diet management in congenital diarrheas and enteropathies - general concepts and disease-specific approach, a narrative review.

ABSTRACT: Congenital diarrheas and enteropathies (CODE) are a group of rare, heterogenous, monogenic disorders that lead to chronic diarrhea in infancy. Definitive treatment is rarely available, and supportive treatment is the mainstay. Nutritional management in the form of either specialized formulas, restrictive diet, or parenteral nutrition support in CODE with poor enteral tolerance is the cornerstone of CODE treatment and long-term growth. The evidence to support the use of specific diet regimens and nutritional approaches in most CODE disorders is limited due to the rarity of these diseases and the scant published clinical experience. The goal of this review was to create a comprehensive guide for nutritional management in CODE, based on the currently available literature, disease mechanism, a

SUBMITTER: Avitzur Y 

PROVIDER: S-EPMC11251218 | biostudies-literature | 2024 Jul

REPOSITORIES: biostudies-literature