Severe Features of Systemic Juvenile Idiopathic Arthritis in Patients With Congenital Heart Disease.

ABSTRACT:

Objective

To describe the clinical features of patients with congenital heart disease (CHD) who subsequently developed systemic juvenile idiopathic arthritis (sJIA).

Methods

We conducted a retrospective review of patients diagnosed with CHD and sJIA at our institution. Detailed clinical, laboratory, and radiographic data were collected from the medical record and reviewed with each patient's primary medical team.

Results

Five patients with sJIA and CHD were identified. Each child had a unique cardiac anatomy, but all the patients required surgical repair during the first year of life. Four children had thymectomies at the time of cardiac surgery. Classic signs of sJIA such as fever (n = 5), rash (n = 5), and arthritis (n = 4) developed after surgical intervention in a

SUBMITTER: Aires BP 

PROVIDER: S-EPMC11296918 | biostudies-literature | 2024 Aug

REPOSITORIES: biostudies-literature