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Granulomatosis With Polyangiitis Causing Severe Aortic Regurgitation.


ABSTRACT: Cardiac granulomatosis with polyangiitis is a rare necrotizing vasculitis impacting small to medium vessels. We present a case of granulomatosis with polyangiitis causing acute aortic valve regurgitation. Imaging reveals valve thickening, inflammation without destruction. Treatment involves glucocorticoids and rituximab for remission, with consideration of surgery for severe valve disease.

SUBMITTER: Fabre KL 

PROVIDER: S-EPMC11522795 | biostudies-literature | 2024 Oct

REPOSITORIES: biostudies-literature