Tracheobronchomalacia is common in children with primary ciliary dyskinesia-A case note review.

ABSTRACT:

Background

The estimated prevalence of tracheobronchomalacia (TBM) in children is about 1:2100. Prevalence of intrathoracic malacia is higher in children with chronic lung disease such as bronchiectasis and cystic fibrosis (CF) and may contribute to increased morbidity.

Objective

To determine the prevalence and assess clinical features of tracheomalacia (TM), TBM and bronchomalacia (BM) in patients with primary ciliary dyskinesia (PCD).

Methods

We performed a retrospective case-note review of all children with a confirmed or highly likely diagnosis of PCD attending Oslo University Hospital between 2000 and 2021. We selected those who had undergone flexible fiberoptic bronchoscopy (FB) and in whom the presence of TBM was assessed. We retrieved demographic and clinical

SUBMITTER: Kennelly SS 

PROVIDER: S-EPMC11600996 | biostudies-literature | 2024 Dec

REPOSITORIES: biostudies-literature