Uveitis in paediatric Behcet disease: a large multicentric Italian cohort.

ABSTRACT:

Background

Behçet disease (BD) is a rare disease in childhood and its uveitis may lead to blindness if not properly treated.

Objectives

We aim to describe a cohort of paediatric BD patients with uveitis.

Design

This is a multicentric retrospective study.

Methods

Six paediatric rheumatology units in Italy were involved including children with a diagnosis of paediatric BD according to the International Criteria for BD Criteria and/or to the International Study Group Criteria for BD, or Paediatric BD classification criteria if they had uveitis. Demographic, laboratory and clinical data were collected and followed up to March 2023. Ocular characteristics and treatment response were assessed according to Standardization Uveitis Nomenclature.

Results

Among the

SUBMITTER: Maccora I 

PROVIDER: S-EPMC11622291 | biostudies-literature | 2024

REPOSITORIES: biostudies-literature