Validation of the PEDiatric Behcet's Disease classification criteria: an evidence-based approach.

ABSTRACT:

Objectives

to validate the PEDiatric Behçet's Disease classification criteria (PEDBD) with an evidence-based approach.

Methods

210 pediatric patients (70 Behçet's disease (BD), 40 Periodic Fever, Aphthous stomatitis, Pharyngitis, Adenitis, 35 familial Mediterranean fever, 26 hyper-IgD syndrome, 22 TNF-Receptor associated Periodic fever Syndrome, 17 undefined recurrent fevers) were randomly selected from the Eurofever Registry. A set of 11 experienced clinicians/researchers blinded to the original diagnosis evaluated the patients. Using the table consensus as gold standard (agreement ≥ 80%), the PEDBD, ISG and ICBD criteria were applied to BD patients and to confounding diseases with other autoinflammatory conditions in order to define their sensitivity, specificity and accur

SUBMITTER: Matucci-Cerinic C 

PROVIDER: S-EPMC11636558 | biostudies-literature | 2023 Nov

REPOSITORIES: biostudies-literature