A very rare phenotype of immunoglobulin G4-related disease that was manifested as constrictive pericarditis: a case report.

ABSTRACT:

Background

Constrictive pericarditis (CP) can arise from various causes, including post-operative degeneration, tuberculosis, and sequelae of pericarditis. Immunoglobulin (Ig) G4-related disease is a rare but recognized cause of CP. However, the specific mechanisms underlying these aetiologies and pathologies remain unclear.

Case summary

A 67-year-old man presented with a 6-month history of bilateral leg oedema, anorexia, and dyspnoea on exertion. Computed tomography (CT) revealed significant pericardial thickening without calcification, right pleural effusion, and ascites. Echocardiography demonstrated a reduced left ventricular ejection fraction and pericardial thickening. The early diastolic mitral annular tissue velocity (e') was preserved as 11.7 cm/s, despite inferior

SUBMITTER: Ono K 

PROVIDER: S-EPMC11718384 | biostudies-literature | 2025 Jan

REPOSITORIES: biostudies-literature