When the heart and tumours intertwine: pulmonary hypertension associated with a neuroendocrine tumour-a case report.

ABSTRACT:

Background

Pulmonary hypertension caused by extrinsic pulmonary vascular compression secondary to mediastinal neuroendocrine tumours is a very rare condition, posing a diagnostic challenge. There is no clear consensus regarding the best treatment strategy due to the lack of clinical data, leading to poor prognoses for these patients.

Case summary

We present the case of a 38-year-old man hospitalized with signs of pulmonary hypertension and acute heart failure. He had experienced progressive dyspnoea over the 12 months prior to admission. Studies performed at our institution revealed dilation of the right heart chambers with right ventricular systolic dysfunction and pulmonary hypertension. Cardiac tomography showed extrinsic vascular compression, leading to emergency endovas

SUBMITTER: Cortez M 

PROVIDER: S-EPMC11748130 | biostudies-literature | 2025 Jan

REPOSITORIES: biostudies-literature