Polycythemia vera and essential thrombocythemia in children, still a challenge for pediatricians.

ABSTRACT: Polycythemia vera (PV) and essential thrombocythemia (ET) are rare myeloproliferative neoplasms (MPN) in children, adolescents and young adults. No recommendations are available concerning these patients' management. Transposing to children the knowledge established in adult patients is not acceptable. For a better understanding of difficulties encountered by pediatricians and adult hematologists, we conducted a national practice analysis concerning follow-up of patients under 18 diagnosed with ET or PV, in France. Then, we present data from a multicentric, descriptive, retrospective study, including 17 patients with ET or PV, diagnosed under 18, coming from 7 hematopediatric departments in France. Interviewed physicians reported a lack of expertise and theoretical training in the hematolo

SUBMITTER: Picard A 

PROVIDER: S-EPMC11794414 | biostudies-literature | 2025 Feb

REPOSITORIES: biostudies-literature