Unusual presentation of anomalous origin of the right pulmonary artery from the ascending aorta: case report.

ABSTRACT:

Background

Anomalous origin of the right pulmonary artery (AORPA) from the ascending aorta is a rare congenital anomaly, representing approximately 0.12% of all congenital heart defects. Early diagnosis and timely intervention are essential to prevent severe complications such as heart failure and pulmonary vascular disease.

Case presentation

We report a case of a full term neonate presented with respiratory distress and cyanosis. Echocardiography revealed an anomalous right pulmonary artery (RPA) origin from the ascending aorta, a large patent ductus arteriosus (PDA) with right-to-left shunt, and moderate tricuspid regurgitation. Despite initial management with prostaglandin E1 (PGE1) infusion, discontinuation of the drug led to clinical deterioration characterized by sever

SUBMITTER: Elhudairy M 

PROVIDER: S-EPMC11794723 | biostudies-literature | 2025 Feb

REPOSITORIES: biostudies-literature