Idiopathic pulmonary fibrosis in the UK: findings from the British Thoracic Society UK Idiopathic Pulmonary Fibrosis Registry.

ABSTRACT:

Objectives

Idiopathic pulmonary fibrosis (IPF) is a progressive interstitial lung disease (ILD) and the most common idiopathic interstitial pneumonia. The UK IPF Registry was established in 2013 to collect data pertaining to clinical features, therapeutic approaches and outcomes. From February 2023, the Registry expanded to include any ILD with evidence of fibrosis.

Design

The UK IPF Registry is a national, multicentre observational registry, including both prospective and retrospective data of patients with IPF in secondary or tertiary care. Cases eligible for inclusion were those with a diagnosis of IPF, presenting at participating centres from January 2013.

Results

Between January 2013 and February 2023, 5052 IPF cases were registered from 64 participating centres.

SUBMITTER: Fahim A 

PROVIDER: S-EPMC11840905 | biostudies-literature | 2025 Feb

REPOSITORIES: biostudies-literature