Fibrillary Glomerulonephritis: Clinicopathological Characteristics and Outcome-Case Series From a Multicentre Australasian Cohort.

ABSTRACT:

Aim

Fibrillary glomerulonephritis (FGN) is a rare deposition disease with unclear aetiology. There are limited case series of FGN described in the literature. Here, we describe the clinicopathological characteristics and outcomes of a series of 26 patients with FGN diagnosed at an Australian tertiary centre for renal diseases over a decade.

Method(s)

The present study includes 26 patients with biopsy-proven FGN diagnosed between January 2011 and December 2021.

Results

The average age at presentation was 60 years, with a female predominance. The mean creatinine at presentation was 205 μmol/L. Most of the patients had significant proteinuria, with an average 24-h urine protein of 3.76 g. Associated conditions included four patients with autoimmune disease, one patient w

SUBMITTER: Komala MG 

PROVIDER: S-EPMC11949550 | biostudies-literature | 2025 Apr

REPOSITORIES: biostudies-literature