Rosai-Dorfman Disease Case Report.

ABSTRACT:

Introduction

Rosai-Dorfman disease (RDD) is a rare histiocytic disorder that is characterized by the accumulation of histiocytes in various tissues, most commonly the lymph nodes. Cutaneous RDD is a rare presentation, accounting for less than 10% of all RDD cases.

Case presentation

An 18-year-old female presented for the first time with a dome-like lesion over an indurated plaque. Both lesions were biopsied, and findings suggested RDD. The patient was referred to an oncologist with a subsequent positron emission tomography scan showing hypermetabolic subcutaneous uptake on bilateral thighs and bilateral lumbar lesions, likely corresponding to the patient's biopsy-proven histiocytosis in addition to a diffuse increased tracer uptake in the thoracic aorta and atria.

Conclus

SUBMITTER: Altamimi NM 

PROVIDER: S-EPMC12266700 | biostudies-literature | 2025 Jan-Dec

REPOSITORIES: biostudies-literature