Orthodontic Treatment in Patients With Epidermolysis Bullosa (EB)-Clinical Practice Guidelines (CPG).

ABSTRACT:

Background

Epidermolysis bullosa (EB) is a rare genetic condition characterized by skin and mucosal fragility. The clinical phenotype is highly variable. Severe types and subtypes, such as junctional EB (JEB), kindler EB (KEB), and recessive dystrophic EB (RDEB), are considered to present a high risk of oral health problems, including malocclusions. Despite this, the literature on orthodontic treatment in patients with EB is scarce and is limited to a few case reports.

Objective

To provide the users with information on the current best practices for orthodontic and dentofacial orthopedic diagnosis and treatment for patients with EB.

Methods

Current information regarding orthodontic treatment in patients with EB was identified based on a systematic literature review. A

SUBMITTER: Veliz S 

PROVIDER: S-EPMC12406292 | biostudies-literature | 2025 Sep-Oct

REPOSITORIES: biostudies-literature