Reciprocated tachycardias in cardiac laminopathy: a clinical case report.

ABSTRACT:

Background

Cardiac laminopathies, associated with mutations in the LMNA gene, are a rare inherited disorder characterized by a broad range of clinical manifestations. There are currently no data on the association between supraventricular re-entrant tachycardias and LMNA-related cardiomyopathy.

Case summary

A 26-year-old male presented with either wide-QRS tachycardia with a left bundle branch block (LBBB) pattern or narrow QRS tachycardia, as well as a history of palpitations since age 15. Echocardiography showed no overt structural heart disease. Electrophysiological studies confirmed the diagnosis of orthodromic atrioventricular re-entrant tachycardia mediated by a concealed left posterolateral accessory pathway (AP), with transient LBBB and dual AV-node physiology, chara

SUBMITTER: Zhelyakov E 

PROVIDER: S-EPMC12415688 | biostudies-literature | 2025 Sep

REPOSITORIES: biostudies-literature