Epidemiology and Surgical Management of Hirschsprung's Disease in France: A 12-Year Retrospective Analysis (2012-2023).

ABSTRACT:

Aim

Hirschsprung's disease (HSCR) is a congenital disorder of the enteric nervous system, leading to functional intestinal obstruction in neonates and young children. This study aimed to assess the epidemiology and surgical management of HSCR in France over a 12-year period using nationwide data.

Methods

We conducted a retrospective cohort study using the French National Hospital Discharge Database (PMSI), including patients aged 0 to 3 years diagnosed and surgically treated for HSCR between 2012 and 2023.

Results

Among 1512 patients, the average incidence was 17.26 per 100 000 live births. Short-segment disease accounted for 70% of cases, and 78.6% were male. A progressive shift toward minimally invasive techniques was observed, with laparoscopic surgery increasing s

SUBMITTER: Wang XX 

PROVIDER: S-EPMC12420887 | biostudies-literature | 2025 Oct

REPOSITORIES: biostudies-literature