Case Report: Dyke-Davidoff-Masson syndrome resulting from a rare combination of hypoplastic left posterior cerebral artery and ipsilateral fetal-type posterior communicating artery.

ABSTRACT:

Introduction

Dyke-Davidoff-Masson syndrome (DDMS) is a rare neurological disorder characterized by unilateral hemiparesis, facial asymmetry, severe epilepsy, and intellectual disability. While congenital DDMS is predominantly attributed to anterior circulation anomalies [e.g., internal carotid artery (ICA) or middle cerebral artery (MCA) hypoplasia], posterior circulation involvement remains unreported. Here, we present the first documented case of congenital DDMS resulting from a rare combination of hypoplastic left posterior cerebral artery (PCA) and ipsilateral fetal-type posterior communicating artery (FTP).

Case presentation

A 19-year-old male exhibited atypical DDMS manifestations: absence seizures, preserved motor function, and occipitotemporal cognitive deficits (MoC

SUBMITTER: Huang H 

PROVIDER: S-EPMC12455352 | biostudies-literature | 2025

REPOSITORIES: biostudies-literature