Cardiac Magnetic Resonance Imaging in the Evaluation and Management of Scimitar Syndrome.

ABSTRACT:

Background

Scimitar syndrome (ScS) features a partial anomalous pulmonary venous connection to the inferior vena cava, with possible septal defects, right lung hypoplasia, and aortopulmonary collaterals. We hypothesize that cardiac magnetic resonance imaging measurements can elucidate ScS physiology and guide surgical decisions.

Methods

This retrospective cohort study included 26 patients diagnosed with ScS from 2011 to 2022 at Children's Hospital of Philadelphia. Patients with single-ventricle physiology were excluded. Medical records were reviewed for patient characteristics and cardiac magnetic resonance imaging data.

Results

Indexed right ventricular end-diastolic volume (RVEDV) (P = .007) and indexed total shunt volume (P = .029) were significantly

SUBMITTER: Pettit AN 

PROVIDER: S-EPMC12559261 | biostudies-literature | 2025 Sep

REPOSITORIES: biostudies-literature