Isolated unilateral absence of the right pulmonary artery with hemoptysis in adulthood: a case report.

ABSTRACT:

Background

Unilateral absence of the pulmonary artery (UAPA) is a rare congenital anomaly resulting from the failure of the sixth aortic arch to fuse with the pulmonary trunk during embryonic development. In the absence of any congenital cardiac anomalies, it is referred to as isolated UAPA. It is more often right-sided and may be asymptomatic until adult age. The literature regarding isolated UAPA in adults is limited. This paper aims to enhance understanding of UAPA in this age group and improve its management objectives.

Case description

We present a rare case involving a 37-year-old man with hemoptysis and slight stuffiness. Computed tomography angiography (CTA) revealed the absence of the right pulmonary artery, along with marked dilation of the bronchial, intercostal,

SUBMITTER: Wang R 

PROVIDER: S-EPMC12593075 | biostudies-literature | 2025

REPOSITORIES: biostudies-literature