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Dataset Information

Quality of life in patients with hypersensitivity pneumonitis and with idiopathic pulmonary fibrosis in real-life clinical practice.


ABSTRACT:

Background

Interstitial lung diseases (ILDs) significantly impair health-related quality of life (HRQL). While HRQL in idiopathic pulmonary fibrosis (IPF) is well studied, data on hypersensitivity pneumonitis (HP) remain limited despite comparable clinical impacts. This study evaluates HRQL in patients with IPF and HP using the King's Brief Interstitial Lung Disease Questionnaire (K-BILD) and EuroQoL 5-Dimension 5-Level Questionnaire (EQ-5D-5L) and examines factors associated with reduced HRQL.

Methods

This longitudinal, observational study included 153 patients [48 IPF, 105 HP, including 72 fibrotic HP (fHP), of whom 32 had usual interstitial pneumonia (UIP) pattern (fHP + UIP)]. Demographic, anamnestic and clinical data, HRQL, respiratory function, echocardiography paramet

SUBMITTER: Suvorova OA 

PROVIDER: S-EPMC12603526 | biostudies-literature | 2025 Oct

REPOSITORIES: biostudies-literature