Ontology highlight
ABSTRACT: Background
Unilateral absence of a pulmonary artery is a rare congenital abnormality with few reports in the literature demonstrating resultant myocardial ischaemia.Case summary
A 59-year-old presented with acute coronary syndrome (ACS). She was known to have right-sided pulmonary atresia. She was found to have angiographically normal looking coronary arteries but had left circumflex to right lung (via bronchial artery) fistula. Stress echocardiography demonstrated significant ischaemia in that territory, which resolved after coil embolization of the fistula.Discussion
To our knowledge, this is the first reported case of ACS secondary to steal phenomena due to circumflex-pulmonary fistula and treated successfully with coil embolization.
SUBMITTER: Wilkes B
PROVIDER: S-EPMC12693583 | biostudies-literature | 2025 Dec
REPOSITORIES: biostudies-literature