Optimizing surgical management for pulmonary artery sarcoma: A 24-year single-center analysis.

ABSTRACT:

Objective

Pulmonary artery sarcoma (PAS) is a rare and aggressive malignancy often misdiagnosed as chronic thromboembolic pulmonary hypertension. This study aimed to evaluate long-term outcomes after surgical treatment and to compare traditional surgical approaches with an integrated strategy developed at a high-volume center.

Methods

We retrospectively reviewed 31 patients who underwent surgery for PAS at Fuwai Hospital between January 2000 and March 2024. Patients were categorized into 2 groups on the basis of surgical approach: traditional resection versus an integrated strategy involving imaging-guided planning, en bloc resection, selective pulmonary endarterectomy, and vascular reconstruction. Kaplan-Meier survival analysis was performed among 26 patients who survived t

SUBMITTER: Xu H 

PROVIDER: S-EPMC12745008 | biostudies-literature | 2025 Dec

REPOSITORIES: biostudies-literature