Beating-Heart Pulmonary Valve Replacement for Isolated Monocuspid Valve.

ABSTRACT:

Background

A monocuspid pulmonary valve is a rare cardiac anomaly that is most commonly seen in patients with other congenital heart defects. Its isolated occurrence is extremely rare.

Case summary

A 20-year-old woman with a history of congenital heart disease presented with exertional dyspnea and generalized weakness. Imaging revealed severe right ventricular dilation and significant enlargement of the main pulmonary artery. Owing to the high risk of aneurysm rupture, she underwent aneurysmectomy, aneurysmorrhaphy, and pulmonary valve replacement (PVR). The heart was maintained in a beating state throughout the procedure, including during cardiopulmonary bypass without cardioplegic arrest.

Discussion

This case demonstrates the feasibility of performing PVR and aneury

SUBMITTER: Abbasi M 

PROVIDER: S-EPMC12789833 | biostudies-literature | 2025 Oct

REPOSITORIES: biostudies-literature