Cardiovascular magnetic resonance findings in a case of Danon disease.
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ABSTRACT:
SUBMITTER: Piotrowska-Kownacka D
PROVIDER: S-EPMC2683831 | biostudies-literature | 2009 Apr
REPOSITORIES: biostudies-literature
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Cardiovascular magnetic resonance findings in a case of Danon disease.
Piotrowska-Kownacka Dorota D Kownacki Lukasz L Kuch Marek M Walczak Ewa E Kosieradzka Agnieszka A Fidzianska Anna A Krolicki Leszek L
Journal of cardiovascular magnetic resonance : official journal of the Society for Cardiovascular Magnetic Resonance 20090429
Danon disease is a rare X-linked dominant lysosomal glycogen storage disease that can lead to severe ventricular hypertrophy and heart failure. We report a case of Danon disease with cardiac involvement evaluated with cardiovascular magnetic resonance, including late gadolinium enhancement and perfusion studies. ...[more]
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