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Time to focus on outcome assessment tools for childhood vasculitis.


ABSTRACT: Childhood systemic vasculitides are a group of rare diseases with multi-organ involvement and potentially devastating consequences. After establishment of new classification criteria (Ankara consensus conference in 2008), it is now time to establish measures for proper definition of activity and damage in childhood primary vasculitis. By comparison to adult vasculitis, there is no consensus for indices of activity and damage assessment in childhood vasculitis. Assessment of disease activity is likely to become a major area of interest in pediatric rheumatology in the near future. After defining the classification criteria for primary systemic childhood vasculitis, the next step was to perform a validation study using the original Birmingham vasculitis activity score as well as the disease

SUBMITTER: Demirkaya E 

PROVIDER: S-EPMC3192748 | biostudies-literature | 2011 Sep

REPOSITORIES: biostudies-literature