The syndromic multiple odontogenic keratocyst in siblings: A familial study.

ABSTRACT:

Purpose

Our aim is to demonstrate the importance of postoperative assessment and highlight the need for a lifetime follow-up of the patient and the siblings in cases of Nevoid Basal Cell Carcinoma Syndrome (NBCCS).

Materials and methods

Three siblings out of which two were of syndromic multiple odontogenic keratocysts, with multiple basal cell nevae were followed-up for manifestations of NBCCS from year 2001 till date. Two of the patients were treated for multiple bilateral odontogenic keratocysts (OKCs). Familial occurrence of the syndromic multiple odontogenic keratocysts was studied.

Result

Although NBCCS is associated with multiple OKCs, it does not imply that a patient should have more than one cyst at a given point in time, rather it refers to the lifetime histo

SUBMITTER: Kalia V 

PROVIDER: S-EPMC3591029 | biostudies-literature | 2011 Jan

REPOSITORIES: biostudies-literature