Recommendations for screening and detection of connective tissue disease-associated pulmonary arterial hypertension.

ABSTRACT:

Objective

Pulmonary arterial hypertension (PAH) affects up to 15% of patients with connective tissue diseases (CTDs). Previous recommendations developed as part of larger efforts in PAH did not include detailed recommendations for patients with CTD-associated PAH. Therefore, we sought to develop recommendations for screening and early detection of CTD-associated PAH.

Methods

We performed a systematic review of the literature on the screening and diagnosis of PAH in CTD. Using the RAND/University of California, Los Angeles consensus methodology, we developed case scenarios followed by 2 stages of voting. First, international experts from a variety of specialties voted anonymously on the appropriateness of each case scenario. The experts then met face-to-face to discuss and re

SUBMITTER: Khanna D 

PROVIDER: S-EPMC3883571 | biostudies-literature | 2013 Dec

REPOSITORIES: biostudies-literature