Outer retinal structure in best vitelliform macular dystrophy.

ABSTRACT:

Importance

Demonstrating the utility of adaptive optics scanning light ophthalmoscopy (AOSLO) to assess outer retinal structure in Best vitelliform macular dystrophy (BVMD).

Objective

To characterize outer retinal structure in BVMD using spectral-domain optical coherence tomography (SD-OCT) and AOSLO.

Design, setting, and participants

Prospective, observational case series. Four symptomatic members of a family with BVMD with known BEST1 mutation were recruited at the Advanced Ocular Imaging Program research lab at the Medical College of Wisconsin Eye Institute, Milwaukee.

Intervention

Thickness of 2 outer retinal layers corresponding to photoreceptor inner and outer segments was measured using SD-OCT. Photoreceptor mosaic AOSLO images within and around visible

SUBMITTER: Kay DB 

PROVIDER: S-EPMC3968428 | biostudies-literature | 2013 Sep

REPOSITORIES: biostudies-literature