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Hyaline fibromatosis syndrome: cutaneous manifestations.

ABSTRACT: Hyaline fibromatosis syndrome is the current name for clinical manifestations of diseases previously known as "infantile systemic hyalinosis" and "juvenile hyaline fibromatosis". The authors report representative clinical cases of each one of the above subtypes with emphasis on cutaneous manifestations and difficulties for early diagnosis in this syndrome, essentially of multidisciplinary approach.

SUBMITTER: Marques SA 

PROVIDER: S-EPMC4861574 | biostudies-literature | 2016 Apr

REPOSITORIES: biostudies-literature

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Hyaline fibromatosis syndrome: cutaneous manifestations.

Marques Silvio Alencar SA   Stolf Hamilton Ometto HO   Polizel Juliana Ocanha JO   Munhoz Tânia T   Brandão Marcela Calixto MC   Marques Mariangela Esther Alencar ME  

Anais brasileiros de dermatologia 20160401 2

Hyaline fibromatosis syndrome is the current name for clinical manifestations of diseases previously known as "infantile systemic hyalinosis" and "juvenile hyaline fibromatosis". The authors report representative clinical cases of each one of the above subtypes with emphasis on cutaneous manifestations and difficulties for early diagnosis in this syndrome, essentially of multidisciplinary approach. ...[more]

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