Ophthalmic manifestations in IgG4-related disease: Clinical presentation and response to treatment in a French case-series.

ABSTRACT: IgG4-related disease (IgG4-RD) is characterized by variable tissue or organ involvements sharing common pathological findings. Orbital or orbital adnexa involvement of the disease has been reported in a few case series. The aim of our study was to characterize and analyze ophthalmic manifestations from a nationwide French case-series.Patients with IgG4-RD and orbital or orbital adnexa involvement included in the French multicentric IgG4-RD case-registry were identified. Only patients fulfilling "modified" comprehensive diagnostic criteria with pathological documentation were retained for the study. Clinical, biological, pathological, radiological findings and data regarding the response to treatment were retrospectively analyzed.According to our data registry, the frequency of IgG4-related

SUBMITTER: Ebbo M 

PROVIDER: S-EPMC5348160 | biostudies-literature | 2017 Mar

REPOSITORIES: biostudies-literature