Computed tomography in adult patients with primary ciliary dyskinesia: Typical imaging findings.

ABSTRACT:

Objectives

Among patients with non-cystic fibrosis bronchiectasis, 1-18% have an underlying diagnosis of primary ciliary dyskinesia (PCD) and it is suspected that there is under-recognition of this disease. Our intention was to evaluate the specific features of PCD seen on computed tomography (CT) in the cohort of bronchiectasis in order to facilitate the diagnosis.

Materials and methods

One hundred and twenty-one CTs performed in patients with bronchiectasis were scored for the involvement, type, and lobar distribution of bronchiectasis, bronchial dilatation, and bronchial wall thickening. Later, associated findings such as mucus plugging, tree in bud, consolidations, ground glass opacities, interlobular thickening, intralobular lines, situs inversus, emphysema, mosaic atte

SUBMITTER: Dettmer S 

PROVIDER: S-EPMC5800555 | biostudies-literature | 2018

REPOSITORIES: biostudies-literature