Contemporary survival of patients with pulmonary arterial hypertension and congenital systemic to pulmonary shunts.

ABSTRACT:

Objective

To compare survival of patients with newly diagnosed pulmonary arterial hypertension associated with congenital heart disease (PAH-CHD) according to various clinical classifications with classifications of anatomical-pathophysiological systemic to pulmonary shunts in a single-center cohort.

Methods

All prevalent cases of PAH-CHD with hemodynamic confirmation by cardiac catheterization in 1995-2015 were retrospectively reviewed. Patients who were younger than three months of age, or with single ventricle following surgery were excluded. Baseline characteristics and clinical outcomes were retrieved from the database. The survival analysis was performed at the end of 2016. Prognostic factors were identified using multivariate analysis.

Results

A total of 366 co

SUBMITTER: Vijarnsorn C 

PROVIDER: S-EPMC5903600 | biostudies-literature | 2018

REPOSITORIES: biostudies-literature