Exquisite response to intravenous immunoglobulin in Susac syndrome during pregnancy.

ABSTRACT:

Introduction

From its initial report on two female patients in 1979 by J.O. Susac, Susac syndrome (SuS) or SICRET (small infarctions of cochlear, retinal and encephalic tissue) has persisted as an elusive entity. To date the available evidence for its treatment is based on case reports and case series. The largest systematic review described only 304 reported cases since the 1970s. Here we presented the first reported case to our knowledge in Mexican population and the unusual presentation in a pregnant patient.

Case presentation

A 34-year-old Hispanic woman was brought to the ER in our hospital for apathy and behavioral changes. Upon arrival at the ER, her husband described a one-month history of behavioral changes with apathy, progressive abulia, visuospatial disorientatio

SUBMITTER: Gomez-Figueroa E 

PROVIDER: S-EPMC5933996 | biostudies-literature | 2018 Mar

REPOSITORIES: biostudies-literature