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Orofacial strength, dysarthria, and dysphagia in congenital myotonic dystrophy.

ABSTRACT: INTRODUCTION:Herein we present an exploratory study of orofacial function in children with congenital myotonic dystrophy (CDM) vs. healthy controls. METHODS:We evaluated 41 children with CDM and 29 healthy controls for speech and swallow function and for lingual and labial strength. RESULTS:The Iowa Oral Performance Instrument (IOPI), measuring tongue strength, and a lip force meter (LFM), measuring lip strength, had excellent interrater reliability with intraclass correlation coefficients (ICCs) of 0.75 (n?=?19, P?

SUBMITTER: Berggren KN 

PROVIDER: S-EPMC6131032 | biostudies-literature | 2018 Sep

REPOSITORIES: biostudies-literature

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Orofacial strength, dysarthria, and dysphagia in congenital myotonic dystrophy.

Berggren Kiera N KN   Hung Man M   Dixon Melissa M MM   Bounsanga Jerry J   Crockett Becky B   Foye Mary D MD   Gu Yushan Y   Campbell Craig C   Butterfield Russell J RJ   Johnson Nicholas E NE  

Muscle & nerve 20180901 3

<h4>Introduction</h4>Herein we present an exploratory study of orofacial function in children with congenital myotonic dystrophy (CDM) vs. healthy controls.<h4>Methods</h4>We evaluated 41 children with CDM and 29 healthy controls for speech and swallow function and for lingual and labial strength.<h4>Results</h4>The Iowa Oral Performance Instrument (IOPI), measuring tongue strength, and a lip force meter (LFM), measuring lip strength, had excellent interrater reliability with intraclass correlat  ...[more]

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